Treatment consisted of systemic intravenous chemotherapy (6 cycles of vincristine, etoposide, and carboplatin) to treat his left eye retinoblastoma, with an excellent tumor response. ![]() Table 1: International Intraocular Retinoblastoma Classification system for Intraocular Retinoblastoma The final diagnosis was group O/C retinoblastoma according to the International Intraocular Retinoblastoma Classification (IIRC) in the left eye with incidental myelinated nerve fiber layer or CT2a if using the AJCC 8th Edition (needs reference). įigure 1: Fundus picture at presentation showing the nasal retinoblastoma associated with myelinated nerve fibers of the optic nerve Although retinoblastoma infiltration was considered, this area was diagnosed as myelinated fibers of the optic nerve. In addition, in the same eye, the optic disc looked anomalous and hyperemic with the presence of white, relatively sharply, demarcated feather-like structures located in the nerve fiber layer, in the juxtapapillary part of the posterior pole but sparing the foveal avascular zone. There was an area of subretinal fluid and some calcified vitreous seeds around the tumor. A white retinal mass about 3 disc diameters in size was seen inferonasally located about 1 disc diameter inferior to the disc in the left eye. Indirect ophthalmoscopy with 360° scleral depression was performed on both eyes the right eye was normal. The anterior segments were unremarkable with a horizontal corneal diameter of 12 mm and a clear lens bilaterally. During the first examination, intraocular pressures were normal at 10 mmHg in both eyes with sevoflurane induction. A complete ocular evaluation was performed under anesthesia. Available from: Īn 11-month-old white male was referred to the pediatric ocular oncology service for leukocoria which had been noted by the parents when the child looked nasally. Leukocoria from myelinated nerve fibers and retinoblastoma. How to cite this URL: Warda O, Lemaitre S, Anguita R, Sagoo MS, Reddy M A. ![]() How to cite this article: Warda O, Lemaitre S, Anguita R, Sagoo MS, Reddy M A. Keywords: Leukocoria, ocular oncology, retinoblastoma In this case, the association of these two conditions led to early diagnosis of retinoblastoma with successful treatment and good visual outcome. The diagnosis of concomitant myelinated nerve fibers and retinoblastoma group O/C was established. We report the clinical findings and imaging in an 11-month-old male referred to the pediatric ocular oncology service for leukocoria. Source of Support: None, Conflict of Interest: None Omar Warda 1, Stephanie Lemaitre 2, Rodrigo Anguita 2, Mandeep S Sagoo 3, M Ashwin Reddy 4ġ Retinoblastoma Unit, Royal London Hospital, London, UK 2 Retinoblastoma Unit, Royal London Hospital Department of Ophthalmology, Moorfields Eye Hospital, London, UK 3 Retinoblastoma Unit, Royal London Hospital Department of Ophthalmology, Moorfields Eye Hospital NIHR Biomedical Research Centre for Ophthalmology, Moorfields Eye Hospital, University College London Institute of Ophthalmology, London, UK 4 Retinoblastoma Unit, Royal London Hospital NIHR Biomedical Research Centre for Ophthalmology, Moorfields Eye Hospital, University College London Institute of Ophthalmology, London, UK Date of Submission Leukocoria from myelinated nerve fibers and retinoblastoma
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